Neurodegeneration with brain iron accumulation--late onset slowly progressive variant.

نویسندگان

  • Priya V Patil
  • Gajendra Manakshe
  • Dinesh P Mahajan
  • Dattatray B Solanke
  • Tejas Sakale
چکیده

Neurodegeneration with Brain Iron Accumulation (NBIA) is a rare type of neuroaxonal dystrophy that can be familial or sporadic, characterized by progressive extrapyramidal degeneration. We report a case of 23 year old male who presented with cervical dystonia, dysarthria and MRI brain suggestive of characteristic "eye-of-the-tiger" appearance in the globus pallidus.

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عنوان ژورنال:
  • The Journal of the Association of Physicians of India

دوره 59  شماره 

صفحات  -

تاریخ انتشار 2011